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La revue de médecine interne – Vol. 33 – N° S2 – p. AA – Fièvre récurrente: penser à la maladie de Caroli – EM|consulte. C’est une cause rare de cholestase chronique et de lithiases intrahépatiques. Nous rapportons deux cas de maladie de Caroli monolobaire. Request PDF on ResearchGate | Maladie de Caroli monolobaire. À propos de 12 cas | BackgroundCaroli’s disease is the dilatation of the segmental intrahepatic.

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Bowel gas and digestive habits make it difficult to obtain a clear sonogramso a CT scan is a good substitution. Cases have also been found in infants and adults. The diagnosis is suspected on clinical grounds and confirmed through detection of cystic dilatation in the biliary tree through imaging studies.

Articles Cases Courses Quiz. Antibiotics are used for cholangitis. Asphyxiating thoracic dysplasia basal body: Using an ultrasoundtubular dilation of the bile ducts can be seen.

Family studies are necessary to determine if Caroli disease is due to inheritable causes. Read it at Google Books – Find it at Amazon. Collaborative Hypertext of Radiology.


When the intrahepatic bile duct wall has protrusions, it is clearly seen as central dots or a linear streak. Caroli disease Turbo spin echo T2-weighted axial MRI of Caroli disease, showing cystic dilatations of bile ducts shown as white. Intestines Intestinal atresia Duodenal maladiee Meckel’s diverticulum Hirschsprung’s disease Intestinal malrotation Dolichocolon Enteric duplication cyst. Access to the full text of this article requires a subscription. Other search option s Alphabetical list.

When the disease is localized to one hepatic lobe, hepatectomy relieves symptoms and appears to remove the risk of malignancy.

Fibrose hépatique congénitale.

Journal of the Pancreas. Bardet—Biedl syndrome mitotic spindle: Antibiotics are used to treat the inflammation of the bile duct, and ursodeoxycholic acid is used for hepatolithiasis.

GastroenterologyMedical genetics. At the other end of the fibropolycystic disease spectrum are Von Meyenburg complexes, also known as biliary hamartomas which result from discrete foci of ductal plate malformation affecting the smallest bile ducts 5.

Summary and related texts.

Maladie de Caroli monolobaire – EM|consulte

If disease is localised, segmentectomy or lobectomy may be offered. Fe Blog Go ad-free. Differential diagnosis The differential diagnosis should include primary sclerosing cholangitis, isolated polycystic liver disease, and hepatic cystic hamartoma see these termsas well as hepatic and choledochal cysts.


Journal page Archives Contents list. Biliary hamartomas Caroli disease Choledochal cysts Bile duct hamartoma.

Fibrose hépatique congénitale.

Caroli disease is a congenital disorder comprising of multifocal cystic dilatation of segmental intrahepatic bile ducts. Assessment of portal venous hypertension by catheterisation of hepatic vein. Personal information regarding our website’s visitors, including their identity, is confidential.

Most cases of CD are sporadic. Rev Fr Etud Clin Biol. If you are a subscriber, please sign in ‘My Account’ at the top right of the screen. Contact Help Who are we? Epidemiology Clinical presentation Pathology Radiographic features Treatment and prognosis History and etymology Differential diagnosis References Images: