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Surgical treatment of Hirschsprung’s disease at the National Children’s .. Enfermedad de Hirschprung. Fantobal-Rojas A. Constipación crónica en el niño. La enfermedad de Hirschsprung es un trastorno congénito infrecuente (afecta aproximadamente a 1 de cada recién nacidos en EE. UU.) que provoca. El estreñimiento se debe diferenciar de la enfermedad de Hirschsprung y de alteraciones anatómicas y metabólicas. La evaluación clínica incluye una historia.

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Hirschsprung Disease HD or Congenital Megacolon is an anomaly that is characterized mainly for the absence of ganglion cells in the myenteric plexus and submucosal in a variable segment of the intestine.

The child who required a stoma was one enfermrdad three children in the series who suffered from chronic constipation following that pull-through procedure.

It is the most frequent cause of the lower neonatal intestinal obstruction. In reality, however, many of these factors continue to be lacking in the majority of the Caribbean isles resulting in late diagnosis and referral of children with HD.

Support Radiopaedia and see fewer ads. Transanal endorectal pull-through for Hirschsprung’s disease. Progress in management and diagnostics. Rectal lI1yectoll1Y for aganglionic megacoIon. A developmental model and approach.

Long-term outcome after Hirschsprung’s disease: Interestingly, it is almost never seen in premature infants. There is ample evidence that the primary pull-through procedure for HD is safe and effective in most situations, including the neonatal period 8. Reliability of intraoperative frozen sections in the management of Hirschsprung’s disease.


Enfermedad de Hirschsprung (para Padres)

Congenitalmegacolon observation hv Frederick Ruysch. Fourtecn-ycars expcricnce in diagnosis and lrealment. Long-term anorectal function after Duhamel operation for Hirschsprung’s disease. The majority of children presented in the neonatal period 10the rest being referred during infancy 7childhood 8 and adulthood 1. Unable to process the form. While transportation and poor communication systems may indeed be a challenge for the Caribbean, especially in the presence of multiple small islands, a number of factors make routine use of the primary pull-through procedure inappropriate for the Caribbean, if not impossible.

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Between July and Niios27 children were identified with HD. A very small number may present in the adult population 1. West Indian Med J ; 46 Suppl 2: It is then imperative that these children be referred as early as possible for specialist care, and once referred appropriately managed. Hence NEC in the term infant should raise one’s suspicion and a rectal suction biopsy performed to exclude HD The affected segment is of small caliber with proximal dilatation.

False-positive intra-operative frozen sections reported in centres where experienced pathologists are unavailable can have serious consequences With respect to Somme’s 8 finding of using a rectal suction biopsy as a factor contributing to earlier diagnosis, we note the delay in diagnosis of some of the children who hirschsprkng in the neonatal period Table 4.


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Enfermedad de Hirschsprung

During the review of patients’ records in this study, it was clear that a number of children who initially presented in the neonatal period and re-presented later in childhood were being treated for necrotizing enterocolitis NEC in the neonatal period when most likely they were experiencing Hirschsprung’s enterocolitis.

Constipation is a common problem in children throughout the world, and the Caribbean is no exception. Idiopathic Disorders of fecal continence in children.

Ahsense of serotonergic neurons in the aganglionic colon. The diagnostic is supported with studies of the barium enema, anorectal manometry and inmunohistochemestry. Classification, identification, and assessment of surgical treatment of anorectal anomalies.

It is postulated that hypoganglionosis reduced number of ganglion cells handles intestinal pseudo-obstruction 4. Hirschsprung’s disease at the University Hospital of the West Indies.